By Gary M. White, MD
Progressive Symmetric Erythrokeratoderma (PSE) or Gottron's syndrome is a rare disorder of well-demarcated erythematous and hyperkeratotic plaques.
There is the onset in early childhood of symmetrically distributed erythematous and hyperkeratotic plaques on the head, extremities, and buttocks.
Similar entities include erythrokeratodermia variabilis, psoriasis, and pityriasis rubra pilaris.
An 18-year-old man presented with mildly itchy, red, raised scaly lesions over face, neck, trunk, and limbs since he was one year old. Lesions started from trunk and gradually increased in size and number to involve face and limbs till the time of puberty, after which the disease stabilized. The lesions were persistent and non-migratory. There was no seasonal variation and no other family member was involved. Indian J Dermatol 2014;59:317
A 15-year-old boy born of second-degree consanguineous marriage presented with asymptomatic scaly skin lesions on the extremities since 5 years of age. Lesions initially started on dorsum of feet, and gradually progressed to involve knees and hands. These lesions were persistent and nonmigratory. There was no history of similar skin eruptions in the family or siblings. Indian Dermatology Online Journal 2013 : 4 : 347-349
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