OLMSTED SYNDROME

Olmsted syndrome is a rare condition in which a palmoplantar keratoderma is associated with periorificial keratotic plaques and scattered keratotic papules.

Clinical

There is a red, scaly periorificial rash along with a mutilating keratoderma. There may be nail dystrophy and scattered keratotic papules. Other potential findings include alopecia, oral leukokeratoses, onychodystrophy, shortness of stature and laxity of the large joints. Cutaneous malignancies have been seen including plantar squamous cell carcinoma and epithelioma cuniculatum.

References

Olmsted syndrome: Rare occurrence in four siblings. Indian J Dermatol 2016;61:347

Indian J Dermatol 2008;53:93-5

Case Reports in Dermatologic Medicine

Indian J Dermatol 2011;56:591-3

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