KERATOSIS FOLLICULARIS SPINULOSA DECALVANS

By Gary M. White, MD


Keratosis follicularis spinulosa decalvans (KFSD) is an X-linked disorder characterized by widespread hyperkeratotic follicular papules (including keratosis pilaris-like lesions), facial erythema, hypotrichosis and progressive alopecia of the scalp, eyelashes, and eyebrows.

Clinical

Extensive keratosis pilaris associated with scarring alopecia is characteristic. Other features include atopy, PPK, and photophobia.

Treatment

There is no specific treatment for KFSD. Various drugs have been tried to delay scarring alopecia such as isotretinoin and dapsone. Emollients, topical steroid, and keratolytic agents may be tried. Acitretin benefited one patient.

References

Int J Trichology 2013;5:29

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