By Gary M. White, MD

Bazex-Dupré-Christol syndrome (BDCS) is an X-linked dominantly inherited disorder characterized by congenital hypotrichosis, hypohidrosis, follicular atrophoderma, multiple milia and basal cell carcinomas.

(As a reminder, X-linked dominant disorders do not necessarily affect males more than females. All daughters of an affected father will also be affected but none of his sons will be affected--unless the mother is also affected). In addition, the mother of an affected son is also affected.)


A 2 year old girl with congenital hypotrichosis if the scalp and eyebrows along with decreased sweat. Her 3 brothers mother and 3 maternal uncles had similar findings. Exam also showed multiple milia of the nose and cheeks. Arch Argent Pediatr 2015;113(5):e256-e259


Homepage | FAQs | Use of Images | Contact Dr. White

It is not the intention of to provide specific medical advice, diagnosis or treatment. only intends to provide users with information regarding various medical conditions for educational purposes and will not provide specific medical advice. Information on is not intended as a substitute for seeking medical treatment and you should always seek the advice of a qualified healthcare provider for diagnosis and for answers to your individual questions. Information contained on should never cause you to disregard professional medical advice or delay seeking treatment. If you live in the United States and believe you are having a medical emergency call 911 immediately.