APLASIA CUTIS CONGENITA

By Gary M. White, MD

Aplasia cutis congenita


Aplasia cutis congenita (ACC) represents an absence of skin in utero. The scalp is most commonly affected. Often, the area has healed by delivery.

Clinical

A congenital, well circumscribed area of alopecia of the scalp is most common. The skin is often atrophic ("membranous"). If a dense amount of hair is present at the periphery (hair collar sign), the possibility of an underlying meningocele or heterotopic brain tissue should be considered. In severe cases, the child may present with extensive scalp ulceration. Purse-string bunching of the skin around the ulcer may occur [Indian Dermatol Online J 2014;5:103-4].

Treatment

Most lesions are small and do not require intervention. When older, the child may have the lesion removed for cosmesis.

Large, ulcerated lesions may be allowed to heal, although grafting may be done.

Additional Pictures

Aplasia cutis congenita

Courtesy O. Dale Collins, MD
Aplasia cutis congenita

RegionalDerm

Homepage | FAQs | Contact Dr. White


It is not the intention of RegionalDerm.com to provide specific medical advice, diagnosis or treatment. RegionalDerm.com only intends to provide users with information regarding various medical conditions for educational purposes and will not provide specific medical advice. Information on RegionalDerm.com is not intended as a substitute for seeking medical treatment and you should always seek the advice of a qualified healthcare provider for diagnosis and for answers to your individual questions. Information contained on RegionalDerm.com should never cause you to disregard professional medical advice or delay seeking treatment. If you live in the United States and believe you are having a medical emergency call 911 immediately.